Case Reports Barw Medical Journal. 2023
Desmoplastic Small Round Cell Tumor: A Case Report
- 1Hiwa Cancer Hospital Centre, Sulaimani Directorate of Health, Sulaimani, Kurdistan, Iraq
- 2Smart Health Tower, Madam Mittrand, Sulaimani, Kurdistan, Iraq
- 3College of Medicine, University of Sulaimani, Madam Mitterrand Street, Sulaimani, Kurdistan, Iraq
- 4Gastroenterology and Hepatology Teaching Hospital, Sulaimani, Kurdistan, Iraq
- 5Research Center, University of Halabja, Halabja, Kurdistan, Iraq
- Submitted
- 10 Nov 2023
- Accepted
- 7 Feb 2024
- Published
- 28 Dec 2023
- Reads
- 1,201
- Downloads
- 780
- Citations
- 0 Citations are Crossref’s count on 8 November 2026.
doi:10.58742/etbs9n84 Open access CC BY 4.0 licence (opens in a new tab)
Abstract
IntroductionDesmoplastic small round cell tumor (DSRCT) is an ultra-rare and highly aggressive mesenchymal tumor that primarily affects the peritoneum, and to a lesser extent, the visceral organs in the abdominal cavity. This study presents a case of a patient who has been diagnosed with DSRCT and has been managed with VAC-IE chemotherapy.
Case presentationA 43-year-old male presented with a complaint of epigastric pain for 20 days but no other clinical symptoms. A CT scan and an abdominal ultrasound showed multiple lesions in the peritoneum, and biopsies were taken from all the sites. Histological analysis revealed nests of small blue round cells surrounded by an abundant stroma. Immunohistochemistry results confirmed the disease to be a desmoplastic small round cell tumor.
ConclusionThis disease is yet to be fully understood, and the response of our case to VAC-IE chemotherapy has shown promising outcomes. This form of treatment can be further studied to establish and help in finding a treatment with a better prognosis.
Keywords DSRCT VAC-IE chemotherapy Rare abdominal metastasis All subjects
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- Citable now
- Barw Medical Journal. 2023
- Permanent link
- doi.org/10.58742/etbs9n84
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