Barw Barw Medical Journal 2960-1959 2023 09 25 Pulmonary Sequestration and Congenital Pulmonary Airway Malformation (CPAM) 1 Presented as A Left Suprarenal Mass:ACase Report 10.58742/3jagbg31 eng Wirya N. Sabr Smart Health Tower, Madam Mittrand, Sulaimani, Kurdistan, Iraq. wirya.sabr@gmail.com Rawa M. Ali Smart Health Tower, Madam Mittrand, Sulaimani, Kurdistan, Iraq. rawa.ali@gmail.com Ali H. Hasan Smart Health Tower, Madam Mittrand, Sulaimani, Kurdistan, Iraq. ali.hasan@gmail.com Hadeel A. Yasseen College of Medicine, University of Sulaimani, Sulaimani, Kurdistan, Iraq. hadeel.yasseen@gmail.com Dlsoz M. Hussein Smart Health Tower, Madam Mittrand, Sulaimani, Kurdistan, Iraq. dlsoz.hussein@gmail.com Zana B. Najmadden Research Center, University of Halabja, Halabja, Kurdistan, Iraq. zana14@gmail.com Fahmi H. Kakamad University of Suliamni. fahmi.hussein@univsul.edu.iq Berun A. Abdalla Smart Health Tower, Madam Mittrand, Sulaimani, Kurdistan, Iraq. berun.anwer95@gmail.com Sasan M. Ahmed Smart Health Tower, Madam Mittrand, Sulaimani, Kurdistan, Iraq. sasan075@gmail.com Shvan H. Mohammed Kscien Organization, Hamdi Street, Azadi Mall, Sulaimani, Kurdistan, Iraq. shvanh80@gmail.com 2023 08 27 Introduction Pulmonary sequestration is a rare condition accounting for 0.1% to 6% of all congenital lung malformations. The correlation with Congenital Pulmonary Airway Malformation (CPAM) type 1 has not been adequately elucidated. Case presentation From routine fetal sonographic screening, a 20-day-old female baby's ultrasound revealed hydronephrosis with enlargement above the left kidney. Magnetic resonance imaging during a follow-up appointment uncovered a left suprarenal lesion of approximately 30 mm, which was not suspected to be adrenal neuroblastoma. After resection, histological analysis was consistent with pulmonary sequestration and confirmed the connection with CPAM type 1. Conclusion Surgery remains the only effective therapeutic choice for intra-abdominal pulmonary sequestration. The definitive diagnosis is confirmed through histological examination.