Barw Barw Medical Journal 2960-1959 2023 02 12 Hydatid Cyst in the Pulmonary Artery: A Systematic Review 10.58742/bmj.v1i1.11 eng Dlsoz M. Hussein Smart Health Tower, Madam Mitterrand Street, Sulaimani, Kurdistan, Iraq. dlsoz.hussein@gmail.com Fahmi H. Kakamad College of Medicine, University of Sulaimani, Madam Mitterrand Street, Sulaimani, Kurdistan, Iraq. fahmi.hussein@univsul.edu.iq Bnar J. Hama Amin Smart Health Tower, Madam Mitterrand Street, Sulaimani, Kurdistan, Iraq. bnar.amin@gmail.com Dana H. Baqi College of Medicine, University of Sulaimani, Madam Mitterrand Street, Sulaimani, Kurdistan, Iraq. dana.saeed@gamil.com Soran H. Tahir College of Medicine, University of Sulaimani, Madam Mitterrand Street, Sulaimani, Kurdistan, Iraq. soran.tahir@univsul.edu.iq Abdulwahid M. Salih College of Medicine, University of Sulaimani, Madam Mitterrand Street, Sulaimani, Kurdistan, Iraq. abdulwahd.salih@gmail.com Razhan K. Ali Shar Hospital, Sulaimani, Kurdistan, Iraq. razhan.ali@gmail.com Fattah H. Fattah Smart Health Tower, Madam Mitterrand Street, Sulaimani, Kurdistan, Iraq. fattah.fattah@univsul.edu.iq Gasha S. Ahmed Kscien Organization for Scientific Research (Middle East office), Hamid Str, Azadi Mall, Sulaimani, Kurdstan, Iraq. Gasha.Ahmed@gmail.com Berun A. Abdalla Smart Health Tower, Scientific Affairs Department, Madam Mitterrand Street, Sulaimani, Kurdistan, Iraq. berun.anwer95@gmail.com Hussein M. Hamasalih Smart Health Tower, Madam Mitterrand Street, Sulaimani, Kurdistan, Iraq. hussein.hama@gmail.com Hiwa O. Abdullah Smart Health Tower, Scientific Affairs Department, Madam Mitterrand Street, Sulaimani, Kurdistan, Iraq. hiewaom96@gmail.com Sabah J. Hassan Ministry of Health, Sulaimani, Kurdistan, Iraq. sabah.jalal@gmail.com 2023 01 10 Abstract Introduction It is uncommon to have a hydatid cyst in the pulmonary artery. Typically, it results from an intracardiac cyst or a surgical cyst rupturing from a hepatic origin. The objective of this systematic review is to describe this rare disease. Methods The electronic search engine and database "Google Scholar" and "PubMed" were systematically searched for pertinent publications in the English language. Results A total of 45 papers were initially found by the systematic search; however, only 16 studies that comprised 16 patients were included. Eight (50%) of the patients were male and eight (50%) were female. Hemoptysis, dyspnea, bloody sputum, vomiting, and shortness of breath were the clinically significant symptoms. Twelve (75%) of the patients had a history of hepatic hydatid disease, followed by three patients (18.8%) with primary lung cystic lesions, and one (6.3%) patient with primary cardiac lesions. Severe pulmonary hypertension, septic shock, and massive hemoptysis all contributed to the death of three (18.8%) patients. Conclusion Localization of hydatid cysts inside the pulmonary artery is incredibly uncommon but life-threatening condition. Surgery may be the last remaining choice for some patients.